Pathways of ammonia detoxification to GLN in muscles connected to enhanced consumption of the BCAA and ?-KG (cataplerosis) and proposed results of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Good influence of BCAA on ammonia detoxification to GLN can be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbutyr